Pediatric bone marrow:
Gespeichert in:
1. Verfasser: | |
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Format: | Buch |
Sprache: | English |
Veröffentlicht: |
Berlin [u.a.]
Springer
2004
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Schlagworte: | |
Online-Zugang: | Inhaltsverzeichnis |
Beschreibung: | Literaturangaben |
Beschreibung: | XII, 296 S. Ill., graph. Darst. |
ISBN: | 3540442057 |
Internformat
MARC
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100 | 1 | |a Penchansky, Lila |e Verfasser |4 aut | |
245 | 1 | 0 | |a Pediatric bone marrow |c Lila Penchansky |
264 | 1 | |a Berlin [u.a.] |b Springer |c 2004 | |
300 | |a XII, 296 S. |b Ill., graph. Darst. | ||
336 | |b txt |2 rdacontent | ||
337 | |b n |2 rdamedia | ||
338 | |b nc |2 rdacarrier | ||
500 | |a Literaturangaben | ||
650 | 4 | |a Kind - Knochenmarkkrankheit | |
650 | 4 | |a Kind | |
650 | 4 | |a Bone Marrow Diseases |x diagnosis |x Child | |
650 | 4 | |a Bone marrow |x Diseases |x Diagnosis | |
650 | 4 | |a Children |x Diseases |x Diagnosis | |
650 | 4 | |a Leukemia in children |x Diagnosis | |
650 | 4 | |a Pediatrics | |
650 | 0 | 7 | |a Kind |0 (DE-588)4030550-8 |2 gnd |9 rswk-swf |
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Datensatz im Suchindex
_version_ | 1804130509395066880 |
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adam_text | Chapter 1
Normal Bone Marrow 1
References 13
Chapter 2
Inherited Bone Marrow Failure 15
Introduction 15
Inherited Hematopoietic Syndromes
Associated with Pancytopenia 15
Fanconi Anemia 15
=0 Laboratory Findings 16
Dyskeratosis Congenita 18
o Laboratory Findings 18
Shwachman Diamond Syndrome 18
o Laboratory Findings 18
Congenital Amegakaryocytic
Thrombocytopenia 19
o Laboratory Findings 19
Rare Familial Marrow Failure Syndromes... 19
Inherited Hematopoietic Syndromes
Associated with Single Cytopenia 19
Diamond Blackfan Anemia 19
= Laboratory Findings 19
Congenital Dyserythropoietic Anemias 20
Severe Congenital Neutropenia 24
= Laboratory Findings 24
Cyclic Neutropenia 27
= Laboratory Findings 27
Chronic Benign Neutropenia 28
Thrombocytopenia with Absent Radii 28
= Laboratory Findings 28
Inherited Disorders of the Leukocytes
Associated with Change in their Morphology... 29
Pelger Hiiet Anomaly 29
j
May Hegglin Anomaly 29
Che diak Higashi Syndrome 30
Alder Reilly Anomaly 32
Other Morphological Abnormalities 32
Inherited Immunodeficiency 34
Reticular Dysgenesis
(Alymphocytic Neutropenia) 34
= Laboratory Findings 34
X Linked Agammaglobulinemia
(Bruton Agammaglobulinemia) 35
o Laboratory Findings 35
Cartilage Hair Hypoplasia 35
¦5 Laboratory Findings 35
Wiskott Aldrich Syndrome 35
¦ o Laboratory Findings 36
Omenn Syndrome 36
=0 Laboratory Findings 36
Inherited Sideroblastic Anemias 36
= Laboratory Findings 37
8 Aminolevulinate Synthase (ALAS2)
Deficiency 38
Pearson Syndrome 38
Osteopetrosis 38
^ Laboratory Findings 39
References 41
Chapter 3
Macrophage and Dendritic Cell Related
Disorders Including the Lysosomal
Storage Disorders 47
Introduction 47
Storage Disorders 48
Gaucher Disease 48
= Laboratory Findings 48
Niemann Pick Disease 50
=5 Laboratory Findings 50
Contents
Wolman Disease 52
Fabry Disease 52
Sialidoses 52
Gangliosidosis GMl and GM2 53
Fucosidosis 53
OC Mannosidosis 53
Glycogen Storage Diseases 54
Mucopolysaccharidosis 54
Cystinosis 55
Primary Hyperoxaluria 55
Sea blue Histiocytosis 55
Histiocytosis 57
Langerhans Cell Histiocytosis 59
o Laboratory Findings 61
Xanthoma Disseminatum 62
Macrophage Related Disorders 64
Hemophagocytic Syndrome 64
^ Laboratory Findings 68
References 68
Chapter 4
Bone Marrow Infections 71
Introduction 71
Infection Associated
Hemophagocytic Syndrome 72
Granulomas 72
Bacterial Infections 72
Mycobacteria 75
Ehrlichiosis 77
Fungus ¦] /
Viruses 80
Human Parvovirus B19 81
Epstein Barr Virus 85
Cytomegalovirus 88
Human Immune Deficiency Virus 89
Human Herpesvirus Type 6 92
Other Viruses 94
Parasites 95
Malaria 95
Other Parasites 96
References 97
Chapter 5
Bone Marrow Metastases 101
Introduction 101
= Laboratory Findings 102
Neuroblastoma 104
= Laboratory Findings 112
Rhabdomyosarcoma 115
^ Laboratory Findings 118
Ewing Family of Tumors 119
¦=» Laboratory Findings 119
Desmoplastic Small Round Cell Tumor 121
Central Nervous System 123
o Laboratory Findings 123
Other Metastatic Tumors 125
References 129
Chapter 6
Hematologic Manifestations of Trisomy 21 .. 133
Introduction 133
o Laboratory Findings 133
Acute Megakaryoblastic Leukemia (FAB M7)... 139
Introduction 139
o Laboratory Findings 139
Cytochemistry
and Immunocytochemistry 142
Electron Microscopy 145
Cytogenetic and Molecular Genetics 145
References 147
Chapter 7
Myelodysplastic Syndromes 151
Myelodysplastic
and Myeloproliferative Disorders 151
Introduction 151
Myelodysplastic Syndromes 152
Juvenile Myelomonocytic Leukemia 152
o Laboratory Findings 153
Monosomy 7 Syndrome 156
Unclassifiable Myelodysplastic Syndromes.. 158
MDSs that Fit the FAB Classification
in Children 159
¦=» Laboratory Findings 161
Myeloproliferative Disorders 162
Chronic Myelogenous Leukemia 162
o Laboratory Findings 163
Chronic Neutrophilic Leukemia 167
Polycythemia Disorders 168
Polycythemia Vera 168
^ Laboratory Findings 168
Essential Thrombocythemia 169
¦= Laboratory Findings 169
Hypereosinophilic Syndrome /
Chronic Eosinophilic Leukemia 170
o Laboratory Findings 172
Systemic Mastocytosis 173
^ Laboratory Findings 174
References 176
Chapter 8
Acute Myeloid Leukemia 179
Introduction 179
Acute Myelogenous Leukemia 180
$ Laboratory Findings 180
Acute Myeloid Leukemia
with Minimal Differentiation (FAB Mo) 182
Acute Myeloid Leukemia
without Maturation (FAB Mi) 184
Acute Myeloid Leukemia with Maturation
(FAB M2) 185
Acute Promyelocytic Leukemia (FAB M3) 189
Acute Myelomonocytic Leukemia (FAB M4) 195
Acute Monoblastic Leukemia (M5) 198
Acute Erythroleukemia (M6) 201
Acute Megakaryoblastic Leukemia (M7) 203
Acute Basophilic Leukemia 203
Minimal Residual Disease 205
Therapy Related Acute Leukemia 205
Congenital Leukemia 207
Recurrent Chromosomal Abnormalities 210
Acute Leukemia of Ambiguous Lineage 211
References 211
Contents
Chapter 9
Acute Lymphoblastic Leukemia
and Lymphoma 215
Introduction 215
Acute Lymphocytic Leukemia /
Lymphoblastic Lymphoma 216
o Laboratory Findings 216
Minimal Residual Disease 237
Lymphomas 237
Non Hodgkin Lymphomas 238
Large Cell Lymphomas 238
Anaplastic Large Cell Lymphoma 239
o Laboratory Findings 239
Hodgkin Lymphoma 241
o Laboratory Findings 241
References 243
Chapter 10
Anemias 247
Introduction 247
Microcytic Anemias 249
Iron Deficiency Anemia 249
o Laboratory Findings 249
Macrocytic Anemias 252
B12 and Folk Deficiency 252
= Laboratory Findings 252
Normocytic Anemias 254
Hemolytic Anemias 255
Hereditary Hemolytic Anemias 258
Red Blood Cell Membrane Disorders 258
Hereditary Spherocytosis 258
^ Laboratory Findings 259
Hereditary Elliptocytosis Syndromes 261
o Laboratory Findings 262
Other Inherited Disorders
of the Red Cell Membrane 264
Hereditary Anemias
Due to Hemoglobin Abnormalities 264
Sickle Cell Anemia 264
=» Laboratory Findings 264
Thalassemia Syndromes 266
(3 Thalassemias 268
= Laboratory Findings 268
oe Thalassemias 268
Contents
Acquired Hemolytic Anemia 269
Hemolytic Disease of Newborn 269
o Laboratory Findings 269
Autoimmune Hemolytic Anemia 270
^ Laboratory Findings 271
Acquired Non Immune Hemolytic Anemias ... 272
Paroxysmal Nocturnal Hemoglobinuria .... 272
Transient Erythroblastopenia of Childhood 272
Aplastic Anemia 273
o Laboratory Findings 273
References 277
Subject Index 281
|
any_adam_object | 1 |
author | Penchansky, Lila |
author_facet | Penchansky, Lila |
author_role | aut |
author_sort | Penchansky, Lila |
author_variant | l p lp |
building | Verbundindex |
bvnumber | BV017815370 |
callnumber-first | R - Medicine |
callnumber-label | RC645 |
callnumber-raw | RC645.7 |
callnumber-search | RC645.7 |
callnumber-sort | RC 3645.7 |
callnumber-subject | RC - Internal Medicine |
classification_rvk | YQ 3500 |
ctrlnum | (OCoLC)249463523 (DE-599)BVBBV017815370 |
dewey-full | 618.9241 |
dewey-hundreds | 600 - Technology (Applied sciences) |
dewey-ones | 618 - Gynecology, obstetrics, pediatrics, geriatrics |
dewey-raw | 618.9241 |
dewey-search | 618.9241 |
dewey-sort | 3618.9241 |
dewey-tens | 610 - Medicine and health |
discipline | Medizin |
format | Book |
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illustrated | Illustrated |
indexdate | 2024-07-09T19:22:10Z |
institution | BVB |
isbn | 3540442057 |
language | English |
oai_aleph_id | oai:aleph.bib-bvb.de:BVB01-010696302 |
oclc_num | 249463523 |
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owner | DE-355 DE-BY-UBR DE-578 |
owner_facet | DE-355 DE-BY-UBR DE-578 |
physical | XII, 296 S. Ill., graph. Darst. |
publishDate | 2004 |
publishDateSearch | 2004 |
publishDateSort | 2004 |
publisher | Springer |
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spelling | Penchansky, Lila Verfasser aut Pediatric bone marrow Lila Penchansky Berlin [u.a.] Springer 2004 XII, 296 S. Ill., graph. Darst. txt rdacontent n rdamedia nc rdacarrier Literaturangaben Kind - Knochenmarkkrankheit Kind Bone Marrow Diseases diagnosis Child Bone marrow Diseases Diagnosis Children Diseases Diagnosis Leukemia in children Diagnosis Pediatrics Kind (DE-588)4030550-8 gnd rswk-swf Knochenmarkkrankheit (DE-588)4228476-4 gnd rswk-swf Kind (DE-588)4030550-8 s Knochenmarkkrankheit (DE-588)4228476-4 s DE-604 HBZ Datenaustausch application/pdf http://bvbr.bib-bvb.de:8991/F?func=service&doc_library=BVB01&local_base=BVB01&doc_number=010696302&sequence=000002&line_number=0001&func_code=DB_RECORDS&service_type=MEDIA Inhaltsverzeichnis |
spellingShingle | Penchansky, Lila Pediatric bone marrow Kind - Knochenmarkkrankheit Kind Bone Marrow Diseases diagnosis Child Bone marrow Diseases Diagnosis Children Diseases Diagnosis Leukemia in children Diagnosis Pediatrics Kind (DE-588)4030550-8 gnd Knochenmarkkrankheit (DE-588)4228476-4 gnd |
subject_GND | (DE-588)4030550-8 (DE-588)4228476-4 |
title | Pediatric bone marrow |
title_auth | Pediatric bone marrow |
title_exact_search | Pediatric bone marrow |
title_full | Pediatric bone marrow Lila Penchansky |
title_fullStr | Pediatric bone marrow Lila Penchansky |
title_full_unstemmed | Pediatric bone marrow Lila Penchansky |
title_short | Pediatric bone marrow |
title_sort | pediatric bone marrow |
topic | Kind - Knochenmarkkrankheit Kind Bone Marrow Diseases diagnosis Child Bone marrow Diseases Diagnosis Children Diseases Diagnosis Leukemia in children Diagnosis Pediatrics Kind (DE-588)4030550-8 gnd Knochenmarkkrankheit (DE-588)4228476-4 gnd |
topic_facet | Kind - Knochenmarkkrankheit Kind Bone Marrow Diseases diagnosis Child Bone marrow Diseases Diagnosis Children Diseases Diagnosis Leukemia in children Diagnosis Pediatrics Knochenmarkkrankheit |
url | http://bvbr.bib-bvb.de:8991/F?func=service&doc_library=BVB01&local_base=BVB01&doc_number=010696302&sequence=000002&line_number=0001&func_code=DB_RECORDS&service_type=MEDIA |
work_keys_str_mv | AT penchanskylila pediatricbonemarrow |