36th Hemophilia Symposium: Hamburg 2005
Gespeichert in:
| Körperschaft: | |
|---|---|
| Format: | Tagungsbericht Buch |
| Sprache: | English |
| Veröffentlicht: |
Berlin [u.a.]
Springer
2007
|
| Schlagworte: | |
| Online-Zugang: | Inhaltsverzeichnis |
| Beschreibung: | Literaturangaben |
| Beschreibung: | XXXIV, 319 S. Ill., graph. Darst. 24 cm |
| ISBN: | 9783540367147 3540367144 |
Internformat
MARC
| LEADER | 00000nam a2200000 c 4500 | ||
|---|---|---|---|
| 001 | BV022306828 | ||
| 003 | DE-604 | ||
| 005 | 20080702 | ||
| 007 | t | ||
| 008 | 070312s2007 gw ad|| |||| 10||| eng d | ||
| 015 | |a 06,N35,0745 |2 dnb | ||
| 015 | |a 07,A09,1234 |2 dnb | ||
| 016 | 7 | |a 980745594 |2 DE-101 | |
| 020 | |a 9783540367147 |c kart. : EUR 149.75 (freier Pr.), sfr 237.00 (freier Pr.) |9 978-3-540-36714-7 | ||
| 020 | |a 3540367144 |c kart. : EUR 149.75 (freier Pr.), sfr 237.00 (freier Pr.) |9 3-540-36714-4 | ||
| 024 | 3 | |a 9783540367147 | |
| 028 | 5 | 2 | |a 11761495 |
| 035 | |a (OCoLC)180941273 | ||
| 035 | |a (DE-599)BVBBV022306828 | ||
| 040 | |a DE-604 |b ger |e rakddb | ||
| 041 | 0 | |a eng | |
| 044 | |a gw |c XA-DE-BE | ||
| 049 | |a DE-12 |a DE-19 |a DE-355 | ||
| 082 | 0 | |a 616.1572 |2 22/ger | |
| 084 | |a YC 2905 |0 (DE-625)153205:12911 |2 rvk | ||
| 084 | |a 610 |2 sdnb | ||
| 111 | 2 | |a Hämophilie-Symposion |n 36 |d 2005 |c Hamburg |j Verfasser |0 (DE-588)10159574-8 |4 aut | |
| 245 | 1 | 0 | |a 36th Hemophilia Symposium |b Hamburg 2005 |c ed.: I. Scharrer ... |
| 246 | 1 | 3 | |a Thirty-six Hemophilia Symposium |
| 264 | 1 | |a Berlin [u.a.] |b Springer |c 2007 | |
| 300 | |a XXXIV, 319 S. |b Ill., graph. Darst. |c 24 cm | ||
| 336 | |b txt |2 rdacontent | ||
| 337 | |b n |2 rdamedia | ||
| 338 | |b nc |2 rdacarrier | ||
| 500 | |a Literaturangaben | ||
| 650 | 4 | |a Hemophilia |v Congresses | |
| 650 | 0 | 7 | |a Hämophilie |0 (DE-588)4072214-4 |2 gnd |9 rswk-swf |
| 655 | 7 | |0 (DE-588)1071861417 |a Konferenzschrift |y 2005 |z Hamburg |2 gnd-content | |
| 689 | 0 | 0 | |a Hämophilie |0 (DE-588)4072214-4 |D s |
| 689 | 0 | |5 DE-604 | |
| 700 | 1 | |a Scharrer, Inge |d 1938- |e Sonstige |0 (DE-588)118200992 |4 oth | |
| 856 | 4 | 2 | |m Digitalisierung UB Regensburg |q application/pdf |u http://bvbr.bib-bvb.de:8991/F?func=service&doc_library=BVB01&local_base=BVB01&doc_number=015516716&sequence=000002&line_number=0001&func_code=DB_RECORDS&service_type=MEDIA |3 Inhaltsverzeichnis |
| 999 | |a oai:aleph.bib-bvb.de:BVB01-015516716 | ||
Datensatz im Suchindex
| _version_ | 1804136326884229120 |
|---|---|
| adam_text | Contents
I. Epidemiology
HIV
Infection and Causes of Death in Patients with Hemophilia in Germany
(Year
2004/2005
Survey)
H.
Krebs,
W.
Schramm
on Behalf of the Participating German Hemophilia
Centers
...................................... 3
Development of the German Hemophilia Register
Β. Η
aschberger, J. Hesse, M.
Heiden,
and R. Seitz
............... 15
National Hemophilia Registry- Source of Information about the Quality of
Hemophilia Medical Care in a Developing Country
D. Lighezan, F. Vladareanu, V. Uscatescu,
С
Petrescu,
С
Jinca, D. Mihailov,
M.
Bătăneant,
L. Pop, W.
Schramm,
and M.Serban
............... 16
II. Hemophilia Therapy
-
Management of Bleedings and Inhibitors
Regulation of Factor
VIII
Life-Cycle by Receptors from LDL Receptor
Superfamily
E.L. Saenko
.................................... 23
Update of the Inhibitor-Immunology-Study
I.
Wieland,
С.
Wermes,
В.
Eifrig,
К.
Holstein,
H. Pollmann,
В.
Siegmund,
A.
Nimtz-Talaska,
С.
Niekrens,
R. Eisert, A. Tiede, K. Welte, and K.-W.
Sýkora
34
Therapy of Acquired Hemophilia
- Immunoadsorption
and Rituximab
Treatment for Immunosuppression and Substitution of Coagulation Factors
H.-H. Wolf, A. Harba, O. Dorligschaw, and H.-J.
Schmoll .......... 40
III. Orthopedic Treatment in Hemophiliacs
Osteoporosis and Hemophilia
-
Is there a Correlation and is there a Problem?
A. Kurth
..................................... 51
VI
Contents
Orthopedic Evaluation of the Lower Extremity in
249
Children:
A Multicenter Trial
A. Seuser, and E.
Kusch ............................. 54
Simultaneous Bilateral Total Knee Arthroplasty in
Hémophilie
Arthropathy
H. H. Eickhoff, F. W. Koch, G.
Goldmann,
H.-H. Brackmann,
and J. Oldenburg
................................. 57
Alternative Therapy such as the Acupuncture of the Skull for
Hémophilie
Arthropathy
T. A. Wallny, H.-H. Brackmann, G.
Gunia,
P. Wilbertz, J. Oldenburg,
and Cn. Kraft
................................... 63
Endoprosthetics of Large Joints in Patients Infected with
HIV
B. Habermann, M.
Krause,
I. Scharrer, and A. Kurth
............. 67
IV. Hemostaseologic Diagnostics
Factor
VIII
Methods: Which Assay Principle for which Indication?
D.Peetz
...................................... 71
Global ECAT Survey on Factor
VIII
Inhibitor Testing: Results of an Inter-
Laboratory Pilot Study
P.
Meijer,
H.
Verbruggen,
J. Arnout, and M. Spannagl
............. 75
A Practical Concept for Pre-Operative Identification and Improved
Management of Patients at Risk for Bleeding
J.
Kościelny,
S.
Ziemer,
H.
Radtke,
P. Sinha, A.
Salama,
and H.
Kiesewetter 78
V.
Pediatrie Hemostaseology
Intravascular
Tissue Factor in Cord vs Adult Whole Blood
G. CVIRN, M.
KÖSTENBERGER,
J. KUTSCHERA, U. FERSTL, W.
MUNTEAN,
P. SeDLMAYR,
G. Juergens, and S. Gallistl
........................... 93
Perioperative
Coagulation Screening in Children
-
Reasons and Results
С
Bidlingmaier, F. Sax, and K.
Kurnik
..................... 96
Thrombin
Generation in Children
A. Sif.gemund, S. Horneff, and R. Schobess
................... 101
Contents
VII
VI. Free Lectures
Working-Group of the German Hemophilia Assistants
-
History, Purpose
and Goals
K. Andritschke, H.
Ringkamp
for the Working Group of the German
Hemophilia Assistants
..............................
Ill
The Endogenous Thrombin Potential as a New Parameter for the Peri-
Operative Monitoring in Conjunction with Endo-Prosthetic Supply due to
Hémophilie
Arthropathy
U.
Scholz,
A.
Siegemund,
T.
Siegemund,
and R.
Scholz ............ 114
Identification of Inhibitor Epitopes in Acquired Hemophilia
by Phage Display
Ch.
Königs,
Ch.
Kessel, S.
Scholz,
M.
Krause
, Ι.
Scharrer, and
W.
Kreuz . . 118
Spectrum of Molecular Defects and Mutation Detection rate in Patients
with Mild and Moderate Hemophilia A
N.
Bogdanova, A. Markoff, U.
Nowak-Göttl,
R.
Eisert,
C. Wermes,
H.
Pollmann, A. Todorova, A. Eigel,
В.
Dworniczak, and
J.
Horst...... 129
Recombinant
Factor Vila for Major Surgery in Severe Factor XI Deficiency:
Pharmacodynamic Monitoring Using Thromboelastometry
H. Dehmel, J. Priesack, R. Eisert, and A. Tiede
................. 133
VII.
Poster
a) Hemophilia
Establishment of a Web-Based Documentation System for Quality Assurance
of Hemophilia Treatment in Mecklenburg/Western Pomeranian:
a Pilot Study
B.
Steiner,
P. Bruhn,
B. Berthold,
D.
Hähling, B.
Meyer, A. Grainacher,
F. Herrmann, U. Kyank, B.
Gombért,
С.
Burstein,
and
M.
Freund....... 139
Successful
Angiographie Embolization
of Recurrent Elbow Joint Bleeds
in one Patient with Severe Hemophilia A
R. Klamroth, S.
Gottstein,
E.
Essers,
M. Orlovic, and M. Wilaschek
.... 140
Evaluation of Thrombotic Events in Hemophiliacs Undergoing Major
Orthopaedic Surgery without Thrombosis Prophylaxis
M.
Krause, Ch. von Auer,
A. Kurth, M.
Böhm,
L. Hovy,
and I.
Scharrer . . . 144
Motivating Patients and Parents to Document Treatment Correctly
S.Jenkins
...................................... 147
VIII Contents
Fit for Life Competition: Everyone s a Winner
A. Seuser, G. Auerswald, W. Eberl, S. Gutsche, P.
Böhm,
R.
Klamroth,
and A. Kurme
................................... 150
Blood Borne Infections in Hemophiliacs in a Developing Country. A Single
Center Experience
M. Serban, M. Pop, St. Jenariu, L. Pop,
С
Jinca, D. Mihailov, S. Arghirescu,
M.
Bătăneanţ,
and W.
Schramm ......................... 153
Hemophilia Center Frankfurt
-
Twinning Center for Nairobi/Kenya
W. Miesbach, G. Asmelash, M. Boehm, and I. Scharrer
............ 159
Economic Evaluation of Orthopedic and Surgical Interventions in
Hemophiliacs
-
Not Only Direct Medical Costs Matter
D. Mihailov, M. Serban, R. Badeti, P. Tepeneu, W.
Schramm,
and D. Lighezan
161
b) Inhibitors in Hemophilia
The Occurrence of Factor
VIII
Inhibitor in a Patient with Mild Hemophilia A
during Treatment with
Interferon
for Chronic Hepatitis
С
W.
Miesbach,
В.
Llugaliu,
G. Asmelash, Ch.
von Auer,
and I.
Scharrer .... 171
Severe Hemophilia A Patient with High-Titer Inhibitor, use of TGA in the
Monitoring of Bypassing Therapy
Α.
Hluší,
P.
Nowak,
V. Kŕčová,
and
L.
Slavïk
.................. 173
EUREKA
-
an
European Registry for Orthopedic Surgery in Hemophiliacs
with Inhibitors
A. Kurth
...................................... 175
c) Casuistics
Double Balloon Enteroscopy (DBE) with Argon Plasma Laser Coagulation
(APC) for a Patient with Heyde s Syndrome
A.
Trümmer,
F.Wiedbrauck, and S.Hollerbach
................ 179
Successful Liver Transplantation in a Patient with Anti-Thrombocyte
Antibodies and Severe Hemophilia A
W. Miesbach, C. Zapletal, G.
Asmelash,
В.
Llugalio,
W.
O. Bechstein,
and I. Scharrer
.................................. 184
Peri- and Postoperative Course of
95
Patients with von-Willebrand s
Disease
Ch.
von Auer, K. Lotter,
S.
Heinsdorf,
and I. Scharrer
............ 187
Contents
IX
Pregnancy
in
a
Patient
with Congenital Antithrombin Deficiency
B.
Maak,
L. Kochhan, Ch.
Estel,
and P. Heuchel
................ 190
Successful Inhibitor-Elimination with Rituximab in Acquired Hemophilia A
and a Patient with a Carrier Status for Hemophilia A: Two Case Reports
P.
Lages,
A.
HuTH-KüHNE,
and R.
Zimmermann ................. 195
An Interesting Family Case of von-Willebrand-Syndrome
S.
Gottstein,
R. Schneppenheim,
U. Buddę,
and R. Klamroth
......... 200
Clinical Manifestations of Dysfibrinogenemia in Relation to the Fibrinogen
Gene Mutation
W. Miesbach, V. Catania, M.
Böhm,
Th.
Vigh,
Ch.
von Auer,
and I.
Scharrer .................................. 201
Thrombin Generation in
a Hémophilie
Newborn
P. Fritsch,
D.
Zach,
G.
Cvirn,
К.
Baier,
M.
Köstenberger,
В.
Leschnik,
and W.
Muntean
................................. 203
d)
Diagnostics
Rapid and Sensitive Detection of Heterozygous Deletions of one or more
Exons in Hemophilia A Females by Multiplex PCR and DHPLC Technique
A. Pavlova, J.
Schröder,
D.
Delev,
С
R.
Müller,
E.
Seifried,
and
J.
Oldenburg ................................. 213
Molecular Genetic Analysis in Patients with Inherited Factor V Deficiency
A.Pavlova, D.Delev,E.
Seifried,
and
J.
Oldenburg
.............. 217
Expression Analysis of
С
1
-Inhibitor Mutants Confirms Causality
of Missense Mutations for Hereditary Angioedema
T.
Förster,
C. R.
Müller, and
J.
Oldenburg................... 220
Expression
of the
γ
-Glutamyl
Carboxylase (GGCX) Containing the
Arg485Pro Mutation Found in two Unrelated VKCFD1 Patients
S.
Rost,
A. Fregin, V. Mutucumarana, D. Stafford,
C. R.
Müller,
and J. Oldenburg
................................. 224
Concentration of Soluble Endothelial Protein
С
Receptor (EPCR) in Plasma
in Relation to Age,
Sex, BMI
and Hemostasis Parameters
G. Siegert, P. Goez, H.
Kostka,
S.
Gehrisch,
E.
Kuhlisch,
and
S. M. ScHELLONG
............................... 229
Thrombin Generation
is Age-Dependent in Children as well as in Adults
H. Haidl,
С
Cimenti,
В.
Leschnik,
D.
Zach,
and W.
Muntean
......... 235
Contents
Effects of PFA-100 in
Preoperative
Screening for
von Willebrand
Disease
in
310
Patients
B. Roschitz,
С
Weitzer, M. Lindinger, A. Wirnsberger, S. Gindl,
M.
KösTENBERGER,
and W.
Muntean
....................... 240
Control of Aspirin Effect in Chronic Cardiovascular Patients Using two
Whole Blood Platelet Function Assays: PFA-100 and Multiple Electrode
Aggregometry
K.-W.
von Pape, M.
Dzijan-Horn,
J.
Bohner,
M. Spannagl, H. Weisser,
and A. Calatzis
.................................. 243
e) Miscellaneous
Difficulties in the Interpretation of the Term »Patient-Related« in the Scope
of the Introduction of a Remuneration of Additional Payments According
to the OPS
K. H. Beck, P. Dirschedl, M.
Mohrmann,
and B. Waibel
............ 255
Factor
VIII
as Positive Regulator of Activated Platelets
A. Sturm, A. Obergfell, U. Walter, and R.
Grossmann............. 257
Characterization of Three Novel Mutations in the Sodium Binding Site of
Coagulation Factor X
R. F. Strey, K.
Wulff,
W.
Schröder,
and
F. H.
Herrmann
............ 263
Characterization of a Mutation in the
5
Flanking Region and a Novel IVS7
Splice Site Mutation in a Patient with Severe FVII Deficiency
W.
Schröder,
К.
Wulff,
R. Tech, R. Grempler, A. Ruiz-Saez,
and F. H.
Herrmann................................ 272
On the Molecular Basis of Warfarin Resistance in Rats
M. HOnerberg, S.
Rost,
A. Fregin, H. J.
Pelz,
C. R.
Müller, and
J.
Oldenburg 279
Influence of Factor VHR2 on Endogenous Thrombin Potential and Clinical
Phenotype in Factor
VII
Deficiency
R. F. Strey, A.
Siegemund,
T.
Siegemund,
С.
Schubert, G.
Schuster,
К.
Wulff,
and F. H.
Herrmann................................ 284
Splice Site Mutations Effect on the F8 mRNA Splicing
O. El-Maarri, C. Klein, J.
Junen,
J.
Schröder,
C. R.
Müller, and
J.
Oldenburg 291
Species-Specific Variation of VKORCl-Activity and Resistance to Warfarin
A. Fregin, S.
Rost,
C. R.
Müller, and
J.
Oldenburg .............. 295
Contents
XI
Various Missense Mutations in the
Vitamin
К
Epoxide
Reducíase
Complex
Subunit
1
(VKORCl) Cause Hereditary Coumarin Resistance
C. Geisen, S.
Rost, G.
Spohn, A. Fregin, M. Watzka, D. M. Dimichele, H. Haubelt,
M. Heistinger, J.
Kadar,
В.
Kemkes-Matthes, P.
Lages,
E. Lindhoff-Last,
В.
Luxembourg,
H.
Pollmann, R.
Zimmermann,
C. R.
Müller,
E.
Seifried,
and J.
Oldenburg ................................. 298
Establishment
of an
International Registry
of Patients with Congenital
FXIII Deficiency
V. Ivaskevicius, R. Seitz, H. P.
Kohler,
L.
Muszbek,
R. A. S Ariens,
E.
Seifried,
and J.
Oldenburg ................................. 302
The Impact of Freezing of Plasma Samples, ABO Blood Group and Acute-
Phase Reaction on Detecting Mild Factor
VIII
Deficiency and Increased
Factor
VIII
Levels as a Risk Factor for Venous Thromboembolism
J. Bach, H.
Haubelt, U.
Seyfert, A. Vogt, P. Hoerdt, and P.
Hellstern..... 305
Thrombin
Generation in Severely Obese Children
С
Cimenti,
H.
Mangge,
B. Leschnik, H. Haidl, D.
Zach, and
W
Muntean
.. 310
Subject Index
................................... 315
|
| adam_txt |
Contents
I. Epidemiology
HIV
Infection and Causes of Death in Patients with Hemophilia in Germany
(Year
2004/2005
Survey)
H.
Krebs,
W.
Schramm
on Behalf of the Participating German Hemophilia
Centers
. 3
Development of the German Hemophilia Register
Β. Η
aschberger, J. Hesse, M.
Heiden,
and R. Seitz
. 15
National Hemophilia Registry- Source of Information about the Quality of
Hemophilia Medical Care in a Developing Country
D. Lighezan, F. Vladareanu, V. Uscatescu,
С
Petrescu,
С
Jinca, D. Mihailov,
M.
Bătăneant,
L. Pop, W.
Schramm,
and M.Serban
. 16
II. Hemophilia Therapy
-
Management of Bleedings and Inhibitors
Regulation of Factor
VIII
Life-Cycle by Receptors from LDL Receptor
Superfamily
E.L. Saenko
. 23
Update of the Inhibitor-Immunology-Study
I.
Wieland,
С.
Wermes,
В.
Eifrig,
К.
Holstein,
H. Pollmann,
В.
Siegmund,
A.
Nimtz-Talaska,
С.
Niekrens,
R. Eisert, A. Tiede, K. Welte, and K.-W.
Sýkora
34
Therapy of Acquired Hemophilia
- Immunoadsorption
and Rituximab
Treatment for Immunosuppression and Substitution of Coagulation Factors
H.-H. Wolf, A. Harba, O. Dorligschaw, and H.-J.
Schmoll . 40
III. Orthopedic Treatment in Hemophiliacs
Osteoporosis and Hemophilia
-
Is there a Correlation and is there a Problem?
A. Kurth
. 51
VI
Contents
Orthopedic Evaluation of the Lower Extremity in
249
Children:
A Multicenter Trial
A. Seuser, and E.
Kusch . 54
Simultaneous Bilateral Total Knee Arthroplasty in
Hémophilie
Arthropathy
H. H. Eickhoff, F. W. Koch, G.
Goldmann,
H.-H. Brackmann,
and J. Oldenburg
. 57
Alternative Therapy such as the Acupuncture of the Skull for
Hémophilie
Arthropathy
T. A. Wallny, H.-H. Brackmann, G.
Gunia,
P. Wilbertz, J. Oldenburg,
and Cn. Kraft
. 63
Endoprosthetics of Large Joints in Patients Infected with
HIV
B. Habermann, M.
Krause,
I. Scharrer, and A. Kurth
. 67
IV. Hemostaseologic Diagnostics
Factor
VIII
Methods: Which Assay Principle for which Indication?
D.Peetz
. 71
Global ECAT Survey on Factor
VIII
Inhibitor Testing: Results of an Inter-
Laboratory Pilot Study
P.
Meijer,
H.
Verbruggen,
J. Arnout, and M. Spannagl
. 75
A Practical Concept for Pre-Operative Identification and Improved
Management of Patients at Risk for Bleeding
J.
Kościelny,
S.
Ziemer,
H.
Radtke,
P. Sinha, A.
Salama,
and H.
Kiesewetter 78
V.
Pediatrie Hemostaseology
Intravascular
Tissue Factor in Cord vs Adult Whole Blood
G. CVIRN, M.
KÖSTENBERGER,
J. KUTSCHERA, U. FERSTL, W.
MUNTEAN,
P. SeDLMAYR,
G. Juergens, and S. Gallistl
. 93
Perioperative
Coagulation Screening in Children
-
Reasons and Results
С
Bidlingmaier, F. Sax, and K.
Kurnik
. 96
Thrombin
Generation in Children
A. Sif.gemund, S. Horneff, and R. Schobess
. 101
Contents
VII
VI. Free Lectures
Working-Group of the German Hemophilia Assistants
-
History, Purpose
and Goals
K. Andritschke, H.
Ringkamp
for the Working Group of the German
Hemophilia Assistants
.
Ill
The Endogenous Thrombin Potential as a New Parameter for the Peri-
Operative Monitoring in Conjunction with Endo-Prosthetic Supply due to
Hémophilie
Arthropathy
U.
Scholz,
A.
Siegemund,
T.
Siegemund,
and R.
Scholz . 114
Identification of Inhibitor Epitopes in Acquired Hemophilia
by Phage Display
Ch.
Königs,
Ch.
Kessel, S.
Scholz,
M.
Krause
, Ι.
Scharrer, and
W.
Kreuz . . 118
Spectrum of Molecular Defects and Mutation Detection rate in Patients
with Mild and Moderate Hemophilia A
N.
Bogdanova, A. Markoff, U.
Nowak-Göttl,
R.
Eisert,
C. Wermes,
H.
Pollmann, A. Todorova, A. Eigel,
В.
Dworniczak, and
J.
Horst. 129
Recombinant
Factor Vila for Major Surgery in Severe Factor XI Deficiency:
Pharmacodynamic Monitoring Using Thromboelastometry
H. Dehmel, J. Priesack, R. Eisert, and A. Tiede
. 133
VII.
Poster
a) Hemophilia
Establishment of a Web-Based Documentation System for Quality Assurance
of Hemophilia Treatment in Mecklenburg/Western Pomeranian:
a Pilot Study
B.
Steiner,
P. Bruhn,
B. Berthold,
D.
Hähling, B.
Meyer, A. Grainacher,
F. Herrmann, U. Kyank, B.
Gombért,
С.
Burstein,
and
M.
Freund. 139
Successful
Angiographie Embolization
of Recurrent Elbow Joint Bleeds
in one Patient with Severe Hemophilia A
R. Klamroth, S.
Gottstein,
E.
Essers,
M. Orlovic, and M. Wilaschek
. 140
Evaluation of Thrombotic Events in Hemophiliacs Undergoing Major
Orthopaedic Surgery without Thrombosis Prophylaxis
M.
Krause, Ch. von Auer,
A. Kurth, M.
Böhm,
L. Hovy,
and I.
Scharrer . . . 144
Motivating Patients and Parents to Document Treatment Correctly
S.Jenkins
. 147
VIII Contents
Fit for Life Competition: Everyone's a Winner
A. Seuser, G. Auerswald, W. Eberl, S. Gutsche, P.
Böhm,
R.
Klamroth,
and A. Kurme
. 150
Blood Borne Infections in Hemophiliacs in a Developing Country. A Single
Center Experience
M. Serban, M. Pop, St. Jenariu, L. Pop,
С
Jinca, D. Mihailov, S. Arghirescu,
M.
Bătăneanţ,
and W.
Schramm . 153
Hemophilia Center Frankfurt
-
Twinning Center for Nairobi/Kenya
W. Miesbach, G. Asmelash, M. Boehm, and I. Scharrer
. 159
Economic Evaluation of Orthopedic and Surgical Interventions in
Hemophiliacs
-
Not Only Direct Medical Costs Matter
D. Mihailov, M. Serban, R. Badeti, P. Tepeneu, W.
Schramm,
and D. Lighezan
161
b) Inhibitors in Hemophilia
The Occurrence of Factor
VIII
Inhibitor in a Patient with Mild Hemophilia A
during Treatment with
Interferon
for Chronic Hepatitis
С
W.
Miesbach,
В.
Llugaliu,
G. Asmelash, Ch.
von Auer,
and I.
Scharrer . 171
Severe Hemophilia A Patient with High-Titer Inhibitor, use of TGA in the
Monitoring of Bypassing Therapy
Α.
Hluší,
P.
Nowak,
V. Kŕčová,
and
L.
Slavïk
. 173
EUREKA
-
an
European Registry for Orthopedic Surgery in Hemophiliacs
with Inhibitors
A. Kurth
. 175
c) Casuistics
Double Balloon Enteroscopy (DBE) with Argon Plasma Laser Coagulation
(APC) for a Patient with Heyde's Syndrome
A.
Trümmer,
F.Wiedbrauck, and S.Hollerbach
. 179
Successful Liver Transplantation in a Patient with Anti-Thrombocyte
Antibodies and Severe Hemophilia A
W. Miesbach, C. Zapletal, G.
Asmelash,
В.
Llugalio,
W.
O. Bechstein,
and I. Scharrer
. 184
Peri- and Postoperative Course of
95
Patients with von-Willebrand's
Disease
Ch.
von Auer, K. Lotter,
S.
Heinsdorf,
and I. Scharrer
. 187
Contents
IX
Pregnancy
in
a
Patient
with Congenital Antithrombin Deficiency
B.
Maak,
L. Kochhan, Ch.
Estel,
and P. Heuchel
. 190
Successful Inhibitor-Elimination with Rituximab in Acquired Hemophilia A
and a Patient with a Carrier Status for Hemophilia A: Two Case Reports
P.
Lages,
A.
HuTH-KüHNE,
and R.
Zimmermann . 195
An Interesting Family Case of von-Willebrand-Syndrome
S.
Gottstein,
R. Schneppenheim,
U. Buddę,
and R. Klamroth
. 200
Clinical Manifestations of Dysfibrinogenemia in Relation to the Fibrinogen
Gene Mutation
W. Miesbach, V. Catania, M.
Böhm,
Th.
Vigh,
Ch.
von Auer,
and I.
Scharrer . 201
Thrombin Generation in
a Hémophilie
Newborn
P. Fritsch,
D.
Zach,
G.
Cvirn,
К.
Baier,
M.
Köstenberger,
В.
Leschnik,
and W.
Muntean
. 203
d)
Diagnostics
Rapid and Sensitive Detection of Heterozygous Deletions of one or more
Exons in Hemophilia A Females by Multiplex PCR and DHPLC Technique
A. Pavlova, J.
Schröder,
D.
Delev,
С
R.
Müller,
E.
Seifried,
and
J.
Oldenburg . 213
Molecular Genetic Analysis in Patients with Inherited Factor V Deficiency
A.Pavlova, D.Delev,E.
Seifried,
and
J.
Oldenburg
. 217
Expression Analysis of
С
1
-Inhibitor Mutants Confirms Causality
of Missense Mutations for Hereditary Angioedema
T.
Förster,
C. R.
Müller, and
J.
Oldenburg. 220
Expression
of the
γ
-Glutamyl
Carboxylase (GGCX) Containing the
Arg485Pro Mutation Found in two Unrelated VKCFD1 Patients
S.
Rost,
A. Fregin, V. Mutucumarana, D. Stafford,
C. R.
Müller,
and J. Oldenburg
. 224
Concentration of Soluble Endothelial Protein
С
Receptor (EPCR) in Plasma
in Relation to Age,
Sex, BMI
and Hemostasis Parameters
G. Siegert, P. Goez, H.
Kostka,
S.
Gehrisch,
E.
Kuhlisch,
and
S. M. ScHELLONG
. 229
Thrombin Generation
is Age-Dependent in Children as well as in Adults
H. Haidl,
С
Cimenti,
В.
Leschnik,
D.
Zach,
and W.
Muntean
. 235
Contents
Effects of PFA-100 in
Preoperative
Screening for
von Willebrand
Disease
in
310
Patients
B. Roschitz,
С
Weitzer, M. Lindinger, A. Wirnsberger, S. Gindl,
M.
KösTENBERGER,
and W.
Muntean
. 240
Control of Aspirin Effect in Chronic Cardiovascular Patients Using two
Whole Blood Platelet Function Assays: PFA-100 and Multiple Electrode
Aggregometry
K.-W.
von Pape, M.
Dzijan-Horn,
J.
Bohner,
M. Spannagl, H. Weisser,
and A. Calatzis
. 243
e) Miscellaneous
Difficulties in the Interpretation of the Term »Patient-Related« in the Scope
of the Introduction of a Remuneration of Additional Payments According
to the OPS
K. H. Beck, P. Dirschedl, M.
Mohrmann,
and B. Waibel
. 255
Factor
VIII
as Positive Regulator of Activated Platelets
A. Sturm, A. Obergfell, U. Walter, and R.
Grossmann. 257
Characterization of Three Novel Mutations in the Sodium Binding Site of
Coagulation Factor X
R. F. Strey, K.
Wulff,
W.
Schröder,
and
F. H.
Herrmann
. 263
Characterization of a Mutation in the
5'
Flanking Region and a Novel IVS7
Splice Site Mutation in a Patient with Severe FVII Deficiency
W.
Schröder,
К.
Wulff,
R. Tech, R. Grempler, A. Ruiz-Saez,
and F. H.
Herrmann. 272
On the Molecular Basis of Warfarin Resistance in Rats
M. HOnerberg, S.
Rost,
A. Fregin, H. J.
Pelz,
C. R.
Müller, and
J.
Oldenburg 279
Influence of Factor VHR2 on Endogenous Thrombin Potential and Clinical
Phenotype in Factor
VII
Deficiency
R. F. Strey, A.
Siegemund,
T.
Siegemund,
С.
Schubert, G.
Schuster,
К.
Wulff,
and F. H.
Herrmann. 284
Splice Site Mutations Effect on the F8 mRNA Splicing
O. El-Maarri, C. Klein, J.
Junen,
J.
Schröder,
C. R.
Müller, and
J.
Oldenburg 291
Species-Specific Variation of VKORCl-Activity and Resistance to Warfarin
A. Fregin, S.
Rost,
C. R.
Müller, and
J.
Oldenburg . 295
Contents
XI
Various Missense Mutations in the
Vitamin
К
Epoxide
Reducíase
Complex
Subunit
1
(VKORCl) Cause Hereditary Coumarin Resistance
C. Geisen, S.
Rost, G.
Spohn, A. Fregin, M. Watzka, D. M. Dimichele, H. Haubelt,
M. Heistinger, J.
Kadar,
В.
Kemkes-Matthes, P.
Lages,
E. Lindhoff-Last,
В.
Luxembourg,
H.
Pollmann, R.
Zimmermann,
C. R.
Müller,
E.
Seifried,
and J.
Oldenburg . 298
Establishment
of an
International Registry
of Patients with Congenital
FXIII Deficiency
V. Ivaskevicius, R. Seitz, H. P.
Kohler,
L.
Muszbek,
R. A. S Ariens,
E.
Seifried,
and J.
Oldenburg . 302
The Impact of Freezing of Plasma Samples, ABO Blood Group and Acute-
Phase Reaction on Detecting Mild Factor
VIII
Deficiency and Increased
Factor
VIII
Levels as a Risk Factor for Venous Thromboembolism
J. Bach, H.
Haubelt, U.
Seyfert, A. Vogt, P. Hoerdt, and P.
Hellstern. 305
Thrombin
Generation in Severely Obese Children
С
Cimenti,
H.
Mangge,
B. Leschnik, H. Haidl, D.
Zach, and
W
Muntean
. 310
Subject Index
. 315 |
| any_adam_object | 1 |
| any_adam_object_boolean | 1 |
| author_GND | (DE-588)118200992 |
| author_corporate | Hämophilie-Symposion Hamburg |
| author_corporate_role | aut |
| author_facet | Hämophilie-Symposion Hamburg |
| author_sort | Hämophilie-Symposion Hamburg |
| building | Verbundindex |
| bvnumber | BV022306828 |
| classification_rvk | YC 2905 |
| ctrlnum | (OCoLC)180941273 (DE-599)BVBBV022306828 |
| dewey-full | 616.1572 |
| dewey-hundreds | 600 - Technology (Applied sciences) |
| dewey-ones | 616 - Diseases |
| dewey-raw | 616.1572 |
| dewey-search | 616.1572 |
| dewey-sort | 3616.1572 |
| dewey-tens | 610 - Medicine and health |
| discipline | Medizin |
| discipline_str_mv | Medizin |
| format | Conference Proceeding Book |
| fullrecord | <?xml version="1.0" encoding="UTF-8"?><collection xmlns="http://www.loc.gov/MARC21/slim"><record><leader>01914nam a2200481 c 4500</leader><controlfield tag="001">BV022306828</controlfield><controlfield tag="003">DE-604</controlfield><controlfield tag="005">20080702 </controlfield><controlfield tag="007">t</controlfield><controlfield tag="008">070312s2007 gw ad|| |||| 10||| eng d</controlfield><datafield tag="015" ind1=" " ind2=" "><subfield code="a">06,N35,0745</subfield><subfield code="2">dnb</subfield></datafield><datafield tag="015" ind1=" " ind2=" "><subfield code="a">07,A09,1234</subfield><subfield code="2">dnb</subfield></datafield><datafield tag="016" ind1="7" ind2=" "><subfield code="a">980745594</subfield><subfield code="2">DE-101</subfield></datafield><datafield tag="020" ind1=" " ind2=" "><subfield code="a">9783540367147</subfield><subfield code="c">kart. : EUR 149.75 (freier Pr.), sfr 237.00 (freier Pr.)</subfield><subfield code="9">978-3-540-36714-7</subfield></datafield><datafield tag="020" ind1=" " ind2=" "><subfield code="a">3540367144</subfield><subfield code="c">kart. : EUR 149.75 (freier Pr.), sfr 237.00 (freier Pr.)</subfield><subfield code="9">3-540-36714-4</subfield></datafield><datafield tag="024" ind1="3" ind2=" "><subfield code="a">9783540367147</subfield></datafield><datafield tag="028" ind1="5" ind2="2"><subfield code="a">11761495</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(OCoLC)180941273</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(DE-599)BVBBV022306828</subfield></datafield><datafield tag="040" ind1=" " ind2=" "><subfield code="a">DE-604</subfield><subfield code="b">ger</subfield><subfield code="e">rakddb</subfield></datafield><datafield tag="041" ind1="0" ind2=" "><subfield code="a">eng</subfield></datafield><datafield tag="044" ind1=" " ind2=" "><subfield code="a">gw</subfield><subfield code="c">XA-DE-BE</subfield></datafield><datafield tag="049" ind1=" " ind2=" "><subfield code="a">DE-12</subfield><subfield code="a">DE-19</subfield><subfield code="a">DE-355</subfield></datafield><datafield tag="082" ind1="0" ind2=" "><subfield code="a">616.1572</subfield><subfield code="2">22/ger</subfield></datafield><datafield tag="084" ind1=" " ind2=" "><subfield code="a">YC 2905</subfield><subfield code="0">(DE-625)153205:12911</subfield><subfield code="2">rvk</subfield></datafield><datafield tag="084" ind1=" " ind2=" "><subfield code="a">610</subfield><subfield code="2">sdnb</subfield></datafield><datafield tag="111" ind1="2" ind2=" "><subfield code="a">Hämophilie-Symposion</subfield><subfield code="n">36</subfield><subfield code="d">2005</subfield><subfield code="c">Hamburg</subfield><subfield code="j">Verfasser</subfield><subfield code="0">(DE-588)10159574-8</subfield><subfield code="4">aut</subfield></datafield><datafield tag="245" ind1="1" ind2="0"><subfield code="a">36th Hemophilia Symposium</subfield><subfield code="b">Hamburg 2005</subfield><subfield code="c">ed.: I. Scharrer ...</subfield></datafield><datafield tag="246" ind1="1" ind2="3"><subfield code="a">Thirty-six Hemophilia Symposium</subfield></datafield><datafield tag="264" ind1=" " ind2="1"><subfield code="a">Berlin [u.a.]</subfield><subfield code="b">Springer</subfield><subfield code="c">2007</subfield></datafield><datafield tag="300" ind1=" " ind2=" "><subfield code="a">XXXIV, 319 S.</subfield><subfield code="b">Ill., graph. Darst.</subfield><subfield code="c">24 cm</subfield></datafield><datafield tag="336" ind1=" " ind2=" "><subfield code="b">txt</subfield><subfield code="2">rdacontent</subfield></datafield><datafield tag="337" ind1=" " ind2=" "><subfield code="b">n</subfield><subfield code="2">rdamedia</subfield></datafield><datafield tag="338" ind1=" " ind2=" "><subfield code="b">nc</subfield><subfield code="2">rdacarrier</subfield></datafield><datafield tag="500" ind1=" " ind2=" "><subfield code="a">Literaturangaben</subfield></datafield><datafield tag="650" ind1=" " ind2="4"><subfield code="a">Hemophilia</subfield><subfield code="v">Congresses</subfield></datafield><datafield tag="650" ind1="0" ind2="7"><subfield code="a">Hämophilie</subfield><subfield code="0">(DE-588)4072214-4</subfield><subfield code="2">gnd</subfield><subfield code="9">rswk-swf</subfield></datafield><datafield tag="655" ind1=" " ind2="7"><subfield code="0">(DE-588)1071861417</subfield><subfield code="a">Konferenzschrift</subfield><subfield code="y">2005</subfield><subfield code="z">Hamburg</subfield><subfield code="2">gnd-content</subfield></datafield><datafield tag="689" ind1="0" ind2="0"><subfield code="a">Hämophilie</subfield><subfield code="0">(DE-588)4072214-4</subfield><subfield code="D">s</subfield></datafield><datafield tag="689" ind1="0" ind2=" "><subfield code="5">DE-604</subfield></datafield><datafield tag="700" ind1="1" ind2=" "><subfield code="a">Scharrer, Inge</subfield><subfield code="d">1938-</subfield><subfield code="e">Sonstige</subfield><subfield code="0">(DE-588)118200992</subfield><subfield code="4">oth</subfield></datafield><datafield tag="856" ind1="4" ind2="2"><subfield code="m">Digitalisierung UB Regensburg</subfield><subfield code="q">application/pdf</subfield><subfield code="u">http://bvbr.bib-bvb.de:8991/F?func=service&doc_library=BVB01&local_base=BVB01&doc_number=015516716&sequence=000002&line_number=0001&func_code=DB_RECORDS&service_type=MEDIA</subfield><subfield code="3">Inhaltsverzeichnis</subfield></datafield><datafield tag="999" ind1=" " ind2=" "><subfield code="a">oai:aleph.bib-bvb.de:BVB01-015516716</subfield></datafield></record></collection> |
| genre | (DE-588)1071861417 Konferenzschrift 2005 Hamburg gnd-content |
| genre_facet | Konferenzschrift 2005 Hamburg |
| id | DE-604.BV022306828 |
| illustrated | Illustrated |
| index_date | 2024-07-02T16:57:05Z |
| indexdate | 2024-07-09T20:54:38Z |
| institution | BVB |
| institution_GND | (DE-588)10159574-8 |
| isbn | 9783540367147 3540367144 |
| language | English |
| oai_aleph_id | oai:aleph.bib-bvb.de:BVB01-015516716 |
| oclc_num | 180941273 |
| open_access_boolean | |
| owner | DE-12 DE-19 DE-BY-UBM DE-355 DE-BY-UBR |
| owner_facet | DE-12 DE-19 DE-BY-UBM DE-355 DE-BY-UBR |
| physical | XXXIV, 319 S. Ill., graph. Darst. 24 cm |
| publishDate | 2007 |
| publishDateSearch | 2007 |
| publishDateSort | 2007 |
| publisher | Springer |
| record_format | marc |
| spelling | Hämophilie-Symposion 36 2005 Hamburg Verfasser (DE-588)10159574-8 aut 36th Hemophilia Symposium Hamburg 2005 ed.: I. Scharrer ... Thirty-six Hemophilia Symposium Berlin [u.a.] Springer 2007 XXXIV, 319 S. Ill., graph. Darst. 24 cm txt rdacontent n rdamedia nc rdacarrier Literaturangaben Hemophilia Congresses Hämophilie (DE-588)4072214-4 gnd rswk-swf (DE-588)1071861417 Konferenzschrift 2005 Hamburg gnd-content Hämophilie (DE-588)4072214-4 s DE-604 Scharrer, Inge 1938- Sonstige (DE-588)118200992 oth Digitalisierung UB Regensburg application/pdf http://bvbr.bib-bvb.de:8991/F?func=service&doc_library=BVB01&local_base=BVB01&doc_number=015516716&sequence=000002&line_number=0001&func_code=DB_RECORDS&service_type=MEDIA Inhaltsverzeichnis |
| spellingShingle | 36th Hemophilia Symposium Hamburg 2005 Hemophilia Congresses Hämophilie (DE-588)4072214-4 gnd |
| subject_GND | (DE-588)4072214-4 (DE-588)1071861417 |
| title | 36th Hemophilia Symposium Hamburg 2005 |
| title_alt | Thirty-six Hemophilia Symposium |
| title_auth | 36th Hemophilia Symposium Hamburg 2005 |
| title_exact_search | 36th Hemophilia Symposium Hamburg 2005 |
| title_exact_search_txtP | 36th Hemophilia Symposium Hamburg 2005 |
| title_full | 36th Hemophilia Symposium Hamburg 2005 ed.: I. Scharrer ... |
| title_fullStr | 36th Hemophilia Symposium Hamburg 2005 ed.: I. Scharrer ... |
| title_full_unstemmed | 36th Hemophilia Symposium Hamburg 2005 ed.: I. Scharrer ... |
| title_short | 36th Hemophilia Symposium |
| title_sort | 36th hemophilia symposium hamburg 2005 |
| title_sub | Hamburg 2005 |
| topic | Hemophilia Congresses Hämophilie (DE-588)4072214-4 gnd |
| topic_facet | Hemophilia Congresses Hämophilie Konferenzschrift 2005 Hamburg |
| url | http://bvbr.bib-bvb.de:8991/F?func=service&doc_library=BVB01&local_base=BVB01&doc_number=015516716&sequence=000002&line_number=0001&func_code=DB_RECORDS&service_type=MEDIA |
| work_keys_str_mv | AT hamophiliesymposionhamburg 36thhemophiliasymposiumhamburg2005 AT scharreringe 36thhemophiliasymposiumhamburg2005 AT hamophiliesymposionhamburg thirtysixhemophiliasymposium AT scharreringe thirtysixhemophiliasymposium |