Guide to the evaluation and management of neuromuscular disease:
Saved in:
| Main Author: | |
|---|---|
| Format: | Book |
| Language: | English |
| Published: |
Philadelphia
Hanley & Belfus
1999
|
| Subjects: | |
| Online Access: | Inhaltsverzeichnis |
| Physical Description: | XXI, 165 S. Ill. |
| ISBN: | 1560533013 |
Staff View
MARC
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| 100 | 1 | |a Bach, John R. |e Verfasser |4 aut | |
| 245 | 1 | 0 | |a Guide to the evaluation and management of neuromuscular disease |c John R. Bach |
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| 650 | 4 | |a Neuromuscular Diseases |x diagnosis | |
| 650 | 4 | |a Neuromuscular Diseases |x therapy | |
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Record in the Search Index
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| adam_text | CONTENTS
Preface xi
Glossary xv
CHAPTER I Introduction 1
I. The Nerves and Muscles in Neuromuscular Diseases 1
II. Inheriting Neuromuscular Disease 2
CHAPTER 2 The Natural Histories 5
I. Duchenne Muscular Dystrophy 5
II. Spinal Muscular Atrophy and the Floppy Newborn 12
III. Amyotrophic Lateral Sclerosis 14
IV. Other Conditions 16
V. Consideration of Medical Treatment 18
CHAPTER 3 General Diagnostic and Management Considerations 23
I. Early Establishment of Diagnosis and Genetic Counseling 23
II. Intelligence Assessment 25
III. Nutrition and Gastrointestinal Concerns 26
IV. Monitoring for and Prevention of Cardiac Complications 31
THE EARLY MANAGEMENT STAGES
CHAPTER 4 The Ambulatory Stage 35
I. Early and Informed Counseling and Psychological Support .... 35
II. Exercise 37
III. Early Intervention to Prevent Muscle. Joint, and Chest Wall
Contractures 38
A. The Legs 38
1. Supportive Physical and Occupational Therapy 38
2. Physical Therapy. Leg Splinting, and Standing Supports . 3l)
3. Late Surgery. Bracing, and Physical Therapy 40
4. Early Surgery. Minimal Physical Therapy 43
B. The Arms 44
C. The Lungs and Chest Wall 44
CHAPTER 5 The Wheelchair Use Stage 45
I. Facilitation of Independence in Activities of Daily Living
with Assistive Devices 45
A. Upper Limb Contractures 45
B. Assistive Devices and Optimization of Daily Activities 46
1. Mobility 47
2. Beds and Mattresses 56
3. Bathing and Toileting 58
vlii Contents •
4. Communication and Computer Environmental Control . . 59
5. Service Animals 60
6. Transportation 61
II. Early Prevention or Correction of Spinal Deformity 62
THE STAGE OF PROLONGED MEANINGFUL SURVIVAL
CHAPTER 6 Respiratory Considerations 67
I. Statement of the Problem 67
II. Ventilation vs. Oxygenation Impairment 67
III. What Is Respiratory Failure and When Does It Occur? 69
IV. The Most Common Evaluation Errors:
Evaluation for Oxygenation Rather Than
for Ventilation Impairment 70
A. Misinterpretations of Symptoms 70
B. Inadequate Pulmonary Function Studies 71
C. Failure to Monitor Sleep Appropriately 72
D. Overreliance on Arterial Blood Gases 72
V. The Most Common Treatment Errors: Treatment for
Oxygenation Rather Than for Ventilation Impairment 73
A. Oxygen and Medical Management 73
B. Intubation and Tracheostomy Paradigm Paralysis 74
C. Invasive IPPV and Airway Suctioning 74
VI. The Finances of Mismanagement 80
VII. Patient Evaluation 80
CHAPTER 7 Noninvasive Intervention 89
I. Introduction and Definitions 89
A. CPAP Machines 90
B. Bilevel Positive Airway Pressure (BiPAP) Devices 90
C. Portable Volume cycled Ventilators 93
D. Negative Pressure Body Ventilators (NPBVs) 96
E. Body Ventilators That Apply Pressure Directly
to the Body 100
II. Management Goals in Noninvasive Ventilation 101
A. Maintenance of Pulmonary Compliance 102
B. Glossopharyngeal Breathing 104
C. Cough Flows 105
D. Mechanical Insufflation Exsufflation 107
E. Maintenance of Normal Lung Ventilation
Around the Clock 109
III. Treatment Options and Protocols 109
A. Mouthpiece IPPV 109
B. Nasal IPPV Ill
C. Oral nasal Interfaces 112
D. Indications and Criteria for Use of Noninvasive
Respiratory Aids 113
E. Ventilator Preference 114
F. Conventional Treatment and the Noninvasive Aid Protocol
for Home Care 115
G. Protocol for Tracheostomy Tube Decannulation 116
Contents ix
H. Post decannulation and Critical Care 118
I. The Child with SMA 119
J. Cost and Quality of Life Issues 121
K. Difficulties in Initiating the Use of Noninvasive Aids 121
IV. Conclusion 122
CHAPTER 8 Eating Difficulties and Robotic Solutions 123
I. The Swallowing Phases 123
II. Assessment 124
III. Treatment for Dysphagia 126
A. Early Swallowing Difficulty 126
B. Moderate Swallowing Difficulty and Risk of Aspiration .... 126
C. Severe Swallowing Difficulty and Aspiration 127
D. Dysphagia in Duchenne Muscular Dystrophy 129
IV. Facilitation of ADL Independence with Assistive Devices 129
CHAPTER 9 Employment, Marriage, and Life Satisfaction 131
I. Marriage/Divorce 131
II. Life Satisfaction 133
III. Quality of Life Issues 134
IV. Ventilator Style Preference: Tracheostomy IPPV vs.
Noninvasive Physical Medicine Alternatives 136
V. Social Integration 137
CHAPTER 10 Ethical Considerations 139
References 145
Index 157
|
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| illustrated | Illustrated |
| indexdate | 2024-07-09T19:07:36Z |
| institution | BVB |
| isbn | 1560533013 |
| language | English |
| oai_aleph_id | oai:aleph.bib-bvb.de:BVB01-010028605 |
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| physical | XXI, 165 S. Ill. |
| publishDate | 1999 |
| publishDateSearch | 1999 |
| publishDateSort | 1999 |
| publisher | Hanley & Belfus |
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| spelling | Bach, John R. Verfasser aut Guide to the evaluation and management of neuromuscular disease John R. Bach Philadelphia Hanley & Belfus 1999 XXI, 165 S. Ill. txt rdacontent n rdamedia nc rdacarrier Neuromuscular Diseases diagnosis Neuromuscular Diseases therapy Neuromuscular diseases Neuromuskuläre Krankheit (DE-588)4075332-3 gnd rswk-swf Neuromuskuläre Krankheit (DE-588)4075332-3 s DE-604 HBZ Datenaustausch application/pdf http://bvbr.bib-bvb.de:8991/F?func=service&doc_library=BVB01&local_base=BVB01&doc_number=010028605&sequence=000002&line_number=0001&func_code=DB_RECORDS&service_type=MEDIA Inhaltsverzeichnis |
| spellingShingle | Bach, John R. Guide to the evaluation and management of neuromuscular disease Neuromuscular Diseases diagnosis Neuromuscular Diseases therapy Neuromuscular diseases Neuromuskuläre Krankheit (DE-588)4075332-3 gnd |
| subject_GND | (DE-588)4075332-3 |
| title | Guide to the evaluation and management of neuromuscular disease |
| title_auth | Guide to the evaluation and management of neuromuscular disease |
| title_exact_search | Guide to the evaluation and management of neuromuscular disease |
| title_full | Guide to the evaluation and management of neuromuscular disease John R. Bach |
| title_fullStr | Guide to the evaluation and management of neuromuscular disease John R. Bach |
| title_full_unstemmed | Guide to the evaluation and management of neuromuscular disease John R. Bach |
| title_short | Guide to the evaluation and management of neuromuscular disease |
| title_sort | guide to the evaluation and management of neuromuscular disease |
| topic | Neuromuscular Diseases diagnosis Neuromuscular Diseases therapy Neuromuscular diseases Neuromuskuläre Krankheit (DE-588)4075332-3 gnd |
| topic_facet | Neuromuscular Diseases diagnosis Neuromuscular Diseases therapy Neuromuscular diseases Neuromuskuläre Krankheit |
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